商品属性:
产品名称
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EVC2抗体
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英文名称
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EVC2
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产品规格
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50ul 100ul 200ul
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产品货号
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GOY-01K2822
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产品分类
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抗体 / 一抗
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交叉反应
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Human
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保存条件
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Shipped at 4℃. Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.
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标记
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Unconjugated
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抗体来源
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Rabbit
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抗体类型
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Monoclonal
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研究领域
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细胞生物 细胞膜蛋白
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蛋白细胞定位
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细胞核,细胞浆,细胞膜
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纯化方法
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affinity purified by Protein A
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性状
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Liquid
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浓度
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1mg/ml
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储存液
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0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
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发货地
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上海
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背景资料
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EVC2 is an integral membrane protein that plays a vital role in bone formation and skeletal development. Defects in EVC2 are a cause of Ellis-van Creveld syndrome (EVC), also known as chondroectodermal dysplasia. EVC is an autosomal recessive disorder characterized by the clinical tetrad of chondrodystrophy, polydactyly, ectodermal dysplasia and cardiac anomalies. Patients manifest short-limb dwarfism, short ribs, postaxial polydactyly and dysplastic nails and teeth. Conital heart defects, most commonly an atrioventricular septal defect, are observed in 60% of affected individuals.
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细胞间粘附分子非整合素蛋白3抗体英文名称: CD209/DC-SIGN交叉反应: Human, Mouse, Rat标记: Unconjugated
腺苷酸环化酶2抗体英文名称: ADCY2交叉反应: Human, Mouse, Rat, Chicken, Pig, Cow, Horse, Rabbit, Sheep标记: Unconjugated
磷酸化胰岛素受体底物-1抗体英文名称: phospho-IRS1 (Tyr1229)交叉反应: Human, Mouse, Rat, Chicken, Dog, Pig, Cow, Horse, Rabbit, Sheep标记: Unconjugated
组蛋白去甲基化酶JMJD3抗体英文名称: KDM6B交叉反应: Human, Mouse, Rat, Pig, Cow, Horse, Rabbit, Sheep标记: Unconjugated
ATP依赖解旋酶DDX19A抗体英文名称: DDX19A交叉反应: Human, Mouse, Rat, Hamster标记: Unconjugated
脂联素抗体英文名称: Adiponectin交叉反应: Human, Mouse, Rat, Chicken, Dog, Pig, Cow, Rabbit标记: Unconjugated
耳聋相关常染色体显性遗传5抗体英文名称: DFNA5交叉反应: Human, Mouse, Rat, Dog, Cow, Sheep标记: Unconjugated
核苷转运蛋白ENT2抗体英文名称: ENT2交叉反应: Human, Mouse, Rat标记: Unconjugated
EVC2抗体交叉反应: Human, Mouse, Rat, Chicken, Dog, Pig, Cow, Horse, Rabbit, Goose, Zebrafish, Sheep, GPV, Firefly, Bee, Belt Jellyfish, Fish, GuineaPig, Hamster, Shrimp, Fruit Fly, Goat, Monkey, Cat, Donkey, Duck, Chimpanzee, Arabidopsis Thalian英文名称: Di-Methyl-Histone H3 (Lys79)抗体来源: Rabbit抗体类型: Polyclonal
精子细胞碱性蛋白1样蛋白抗体英文名称: RSBN1L交叉反应: Human, Mouse, Rat, Chicken, Dog, Horse, Rabbit, Sheep标记: Unconjugated
胰腺衍生因子抗体英文名称: FAM3B交叉反应: Human, Mouse, Rat标记: Unconjugated
舞蹈症相关蛋白KALRN抗体英文名称: KALRN交叉反应: Human, Mouse, Rat, Chicken, Dog, Pig, Horse标记: Unconjugated
嘌呤嘧啶核酸内切酶2抗体英文名称: APEX2交叉反应: Human, Mouse, Rat, Dog, Cow标记: Unconjugated
磷酸化谷氨酸受体1抗体英文名称: phospho-GluR1 (Thr840)交叉反应: Human, Mouse, Rat, Chicken, Dog, Pig, Cow, Horse, Rabbit, Sheep标记: Unconjugated
磷酸化一氧化氮合成酶3(内皮型)抗体英文名称: Phospho-eNOS (Ser1176)交叉反应: Human, Mouse, Rat标记: Unconjugated
黄素蛋白氧化还原酶MICAL2抗体英文名称: MICAL2交叉反应: Human, Mouse, Rat, Rabbit标记: Unconjugated