商品属性:
产品名称
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FREM2抗体
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英文名称
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FREM2
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产品规格
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50ul 100ul 200ul
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产品货号
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GOY-01K2656
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产品分类
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抗体 / 一抗
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交叉反应
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Human, Mouse, Rat, Horse, Rabbit
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保存条件
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Shipped at 4℃. Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.
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标记
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Unconjugated
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抗体来源
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Rabbit
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抗体类型
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Monoclonal
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研究领域
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心血管 细胞生物 发育生物学 信号转导
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蛋白细胞定位
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细胞膜
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纯化方法
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affinity purified by Protein A
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性状
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Liquid
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浓度
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1mg/ml
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储存液
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Preservative: 15mM Sodium Azide, Constituents: 1% BSA, 0.01M PBS, pH 7.4
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发货地
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上海
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背景资料
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FREM2 is a 3,169 amino acid single-pass type I membrane protein that localizes to the extracellular side of the cell membrane and contains five Calx-beta domains, as well as 12 CSPG repeats. Functioning as an extracellular matrix protein, FREM2 is required for the maintenance of skin and renal epithelia and is also thought to be involved in epidermal adhesion events. Defects or mutations in the e encoding FREM2, which maps to human chromsome 13, are associated with Fraser syndrome, a multisystem malformation that is characterized by ear abnormalities, conital heart defects and cutaneous syndactyly. FREM2 ts as multiple alternatively spliced isoforms.
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